Compare Train and 3D-4D Left Ventricular Systolic Function in Subjects Suffering From Dystrophy and Healthy Subjects

Steinert's disease is an orphan disease. The prognosis of patients with this disease is conditioned by cardiac involvement. Search an early stage alterations in contractile function in subjects suffering from dystrophy would detect patients at risk of sudden death. The first stage of work is to validate the tools to detect early stage of infringement systolic function in a population of patients with myotonic dystrophy.

Inclusion Criteria:

• patients suffering from muscular dystrophy type 1 followed CHU Poitiers.
• age ≥ 18 years

Exclusion Criteria:

• duration QRS> 120 ms ECG permanent ventricular stimulation
• trouble segmental kinetic obvious to echocardiography in visual analysis