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Muscular dystrophies are neuromuscular disorders with disability. Restrictive pulmonary failure and cardiomyopathy affect prognosis.The investigators aim to establish predictive factors for mortality and morbidity in Intensive care unit (ICU ) and to describe the long term follow up after ICU discharge.
Muscular dystrophies are neuromuscular disorders with disability. Restrictive pulmonary failure and cardiomyopathy affect prognosis. Little is known about morbidity and mortality of patients with muscular dystrophies admitted in intensive care unit (ICU).The investigators aim to describe the spectrum of patients with muscular dystrophies admitted in ICU , to establish predictive factors for ICU mortality and morbidity and to describe the long term follow up after ICU discharge.
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| Measure | Description | Time Frame |
|---|---|---|
| ICU mortality | 1 month |
| Measure | Description | Time Frame |
|---|---|---|
| tracheostomy in ICU | 1 month | |
| predictive factors for re admission in ICU | 1 year | |
| long term survival after ICU stay |
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Inclusion Criteria:
Exclusion Criteria:
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All patients with neuro-muscular disorders admitted in ICU since 2005
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| Name | Affiliation | Role |
|---|---|---|
| abdallah Fayssoil, MDPhD | Raymond Poincare Hospital | Principal Investigator |
| Facility | Status | City | State | ZIP | Country | Contacts |
|---|---|---|---|---|---|---|
| Hopital Raymond Poincare | Garches | 92380 | France |
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| ID | Term |
|---|---|
| D009136 | Muscular Dystrophies |
| D009135 | Muscular Diseases |
| ID | Term |
|---|---|
| D020966 | Muscular Disorders, Atrophic |
| D009140 | Musculoskeletal Diseases |
| D009468 | Neuromuscular Diseases |
| D009422 | Nervous System Diseases |
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| 5 years |
| decline of vital capacity after ICU stay | 2 years |
| D030342 | Genetic Diseases, Inborn |
| D009358 | Congenital, Hereditary, and Neonatal Diseases and Abnormalities |