Admission of Adult-onset Still Disease Patients in the ICU

Admission of Adult-onset Still Disease Patients in the ICU: a French Retrospective Multicentric Study

Since its first description in 1971, diagnosing adult-onset Still's disease (AOSD), a rare multisystemic disorder considered as a multigenic autoinflammatory syndrome, remains challenging. Rarely, AOSD may present severe systemic manifestations and require intensive care. The main purpose of the Stil ICU study is to make the first description of the epidemiology of critically ill AOSD patients. The investigators will use a retrospective cohort study design with dual recruitment strategies: (1) via the AOSD referral centres network and (2) via a French academic medical ICU network.

Inclusion Criteria:

• AOSD (history of newly diagnosed)
• ICU admission between January 2001 and June 2017

Exclusion Criteria:

• adults under protection
• admission in step-down unit