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Retinopathy pigmentosa (which affects about 40,000 patients in France) leads to destruction of the peripheral retina. This condition, often familial, frequently affects young patients. Visual acuity is excellent for a long time, the disease affecting the central macular region only belatedly. On the other hand, the visual field is very quickly narrowed to a central or paracentral zone.
For the patient, knowing the limits of his visual field and learning to adapt is necessary especially when traveling.
The management of these patients is twofold:
The residual field of vision is evaluated by a device at the first appointment at the specialized center. This examination, necessary for the professional, is not informative for the patient. It is sometimes supplemented by the evaluation of the visual field of view (ECVS). The ECVS, done jointly by the orthoptist and the locomotion instructor, consists in evaluating the functional visual field on a horizontal plane at 1m (meter) and 5m, and vertical at 5m. The field of vision of the patient, immobile, is materialized by targets deposited at each limit of the zones seen that it indicates.
The investigators believe that the passing of a visual field on the ground, thanks to the projection of the zones of vision, allows the patient to improve his knowledge on his visual possibilities (and gaps) and thus to make his reeducation more efficient.
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| Label | Type | Description | Intervention Names |
|---|---|---|---|
| evaluation of the visual field on the ground | Experimental | evaluation of the visual field on the ground followed by 10 reeducation sessions |
|
| usual care | No Intervention | control session followed by 10 re-education sessions |
| Name | Type | Description | Arm Group Labels | Other Names |
|---|---|---|---|---|
| evaluation of the visual field on the ground | Other | evaluation of the visual field on the ground |
|
| Measure | Description | Time Frame |
|---|---|---|
| difference in the number of errors committed during a walk between T0 and T2 | difference in the number of errors committed (= number of hurdles, number of "doors" forgotten) during a walk between T0 (before ECVS) and T2 (after ECVS + 10 re-education sessions). | 2 months |
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Exclusion Criteria:
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| ID | Term |
|---|---|
| C537612 | RHYNS syndrome |
| D012174 | Retinitis Pigmentosa |
| ID | Term |
|---|---|
| D015785 | Eye Diseases, Hereditary |
| D005128 | Eye Diseases |
| D058499 | Retinal Dystrophies |
| D012162 | Retinal Degeneration |
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| D012164 |
| Retinal Diseases |
| D030342 | Genetic Diseases, Inborn |
| D009358 | Congenital, Hereditary, and Neonatal Diseases and Abnormalities |